• Home
  • About Us
  • Blog

Pulmonary Hypertension RN

  • What is Pulmonary Hypertension?
    • What is Pulmonary Hypertension?
    • Pulmonary Hypertension Symptoms
    • Types of Pulmonary Hypertension
    • Causes of Pulmonary Hypertension
    • PH vs. PAH
    • Diastolic Heart Failure vs. PAH
    • WHO Group 3 Pulmonary Hypertension, IPF & COPD
    • Pulmonary Veno-Occlusive Disease
    • Hereditary Hemorrhagic Telangiectasia (HHT)
      • Hereditary Hemorrhagic Telangiectasia (HHT) Treatment
    • Functional Classification of Pulmonary Hypertension
    • Congenital Heart Disease
      • Eisenmenger’s Syndrome
      • Update on Management of PAH-CHD
      • Congenital Heart Disease & Sleep Apnea
      • Complex Congenital Heart Disease
      • Atrial Septal Defect and Pulmonary Arterial Hypertension
    • Pediatric Pulmonary Arterial Hypertension
    • Sickle Cell and Pulmonary Hypertension
    • Stimulant Associated Pulmonary Arterial Hypertension
    • Porto-Pulmonary Syndrome
    • Research, Life Expectancy & Prognosis for PH
  • Diagnosing & Monitoring PAH
    • Pulmonary Arterial Hypertension Diagnosis
    • How Am I Doing? Assessing Your PAH.
    • Blood Tests
    • Cardiopulmonary Exercise Test (CPET)
    • CT (Computed Tomography) Scan
    • Echocardiogram: An Overview
    • Echocardiogram: A Detailed Look
    • Pulmonary Function Tests (PFTs)
    • Right Heart Catheterization
    • Six Minute Walk
    • Ventilation Perfusion Scan (VQ Scan)
    • CTEPH
      • CTEPH: WHO Group 4 Pulmonary Hypertension
      • PTE (Pulmonary Thromboendarterectomy) Surgery
      • Adempas used to Treat PAH and CTEPH
  • PAH Treatment
    • Pulmonary Hypertension Centers
    • Pulmonary Hypertension Treatments
    • Continuously Infused Therapies Used to Treat PH
    • Prostanoids for Treatment of PH
    • Adcirca and Revatio Used to Treat Pulmonary Arterial Hypertension (PAH)
    • Adempas used to Treat PAH and CTEPH
    • Tracleer, Letairis, and Opsumit Treatments
    • Oxygen Therapy for Pulmonary Hypertension
    • Salt and Water Restrictions
    • Exercise & PAH
    • Diuretics
    • Blood Thinners
    • Getting the Most Out of PAH Therapy
      • Letairis
      • Opsumit
      • Sildenafil (Revatio)
  • Research
  • FAQ’s
    • Implanted Remodulin Pump, Right Heart Catheterization, PAH & Pregnancy
    • Oral Treatments, Care Centers & Hole in Heart
    • FAQ’s: Altitude, Cold & Allergy Medications
    • FAQ’s: Psoriasis, Idiopathic PAH, Contraceptives & PAH
    • FAQ’s: Causes of Pulmonary Hypertension, Symptom Frequency & Care Centers
    • FAQ: PAH Experts, Pregnancy, Mild PAH & Vacationing
    • FAQ’s: CTEPH, Blood Clots, Corrective Surgery & PAH Care Centers
    • FAQ’s: VQ Scans & PAH Curable?
    • FAQ’s: Mild Pulmonary Hypertension?
    • FAQ’s: Boating, Swimming & Eating with PAH
    • FAQ’s: Borderline Pulmonary Hypertension, Hand Swelling, Children with PAH, Costs

Pulmonary Arterial Hypertension Diagnosis

Making the pulmonary hypertension diagnosis

chest x ray severe pah
CXR from a patient with severe PAH. Yellow arrow shows enlarged right main pulmonary artery. Red arrow shows the enlarged left pulmonary artery.

There are several tests that lead to suspicion of pulmonary arterial hypertension (PAH). When a patient complains of shortness of breath an echocardiogram, or ultrasound of the heart, is usually one of the first tests performed. This test can estimate the pressure in the pulmonary arteries and allows the physician to measure the size of the right ventricle and right atrium. It also allows for physicians to evaluate for other diseases that could cause shortness of breath. An echocardiogram report may list a diagnosis of pulmonary hypertension and state pressures are elevated but this does not make a diagnosis of pulmonary arterial hypertension. The pressures are estimated and there is no way to collect accurate hemodynamic data by ultra sound.

EKG to Diagnose Pulmonary Hypertension
EKG demonstrating increased right ventricular load: a sign of pulmonary hypertension.

 

An EKG or ECG is a test that measures the electrical activity of the heart. This is a common test done for patients with shortness of breath. There is a characterstic pattern of findings in advanced PAH.

A chest XRAY is a basic test that is quick and easy to perform. Every patient with complaints of shortness of breath should have a chest XRAY at some time. In advanced disease, there are characteristic abnormalities on this test.

A CT scan of the chest is another more sophisticated imaging test. Findings of enlarged pulmonary arteries and lack of other significant lung disease would warrant follow up testing to rule out pulmonary hypertension but cannot be used to make the diagnosis.

Pulmonary Function Testing is a group of tests that measure different parts of the lung system’s function. A lung doctor interprets these tests. There is a characterstic pattern that can suggest PAH. Many patients are incorrectly told that they have asthma to explain their shortness of breath. This test can help point the doctor in the correct direction.

A right heart catheterization is the only way to officially diagnosis pulmonary arterial hypertension as it is the only way to accurately directly measure the pressures in the pulmonary arteries and the wedge pressure. Both of these hemodynamic measurements are required for diagnosis. In most cases, treatment for pulmonary hypertension should not be initiated before a right heart catheterization is performed because there are many diseases that mimic pulmonary arterial hypertension and the treatments for PAH can be harmful if used when other diseases are present.

PAH Life Expectancy

PAH Research

Research, Life Expectancy & Prognosis for PH

Major Developments in Pulmonary Hypertension Affecting Prognosis 1.     Approval of

Where to Get Treatment?

CCCs for PAH

Pulmonary Hypertension Centers

Where to get treatment for pulmonary hypertension? Pulmonary arterial hypertension is a

Popular Posts

Exercising After Being Diagnosed With Pulmonary Hypertension.

By Dr. Jeremy Feldman

Being diagnosed with pulmonary hypertension is life changing.  Many patients are scared to exercise or participate in

PAH research

Pulmonary Hypertension Association Registry (PHAR)

By Dr. Jeremy Feldman

A registry is a recording of patients and their characteristics.  The PHAR is the first attempt by the PHA to begin to

good news in pah

 

Disclaimer

Recent Blog Posts

  • In Memoriam:  Greg Ahearn, MD June 16, 2024
  • Sotatercept (Winrevair) Approved! June 1, 2024
  • Disappointing News for Rodatristat Ethyl October 11, 2023

Categories

Archives