• Home
  • About Us
  • Blog

Pulmonary Hypertension RN

  • What is Pulmonary Hypertension?
    • What is Pulmonary Hypertension?
    • Pulmonary Hypertension Symptoms
    • Types of Pulmonary Hypertension
    • Causes of Pulmonary Hypertension
    • PH vs. PAH
    • Diastolic Heart Failure vs. PAH
    • WHO Group 3 Pulmonary Hypertension, IPF & COPD
    • Pulmonary Veno-Occlusive Disease
    • Hereditary Hemorrhagic Telangiectasia (HHT)
      • Hereditary Hemorrhagic Telangiectasia (HHT) Treatment
    • Functional Classification of Pulmonary Hypertension
    • Congenital Heart Disease
      • Eisenmenger’s Syndrome
      • Update on Management of PAH-CHD
      • Congenital Heart Disease & Sleep Apnea
      • Complex Congenital Heart Disease
      • Atrial Septal Defect and Pulmonary Arterial Hypertension
    • Pediatric Pulmonary Arterial Hypertension
    • Sickle Cell and Pulmonary Hypertension
    • Stimulant Associated Pulmonary Arterial Hypertension
    • Porto-Pulmonary Syndrome
    • Research, Life Expectancy & Prognosis for PH
  • Diagnosing & Monitoring PAH
    • Pulmonary Arterial Hypertension Diagnosis
    • How Am I Doing? Assessing Your PAH.
    • Blood Tests
    • Cardiopulmonary Exercise Test (CPET)
    • CT (Computed Tomography) Scan
    • Echocardiogram: An Overview
    • Echocardiogram: A Detailed Look
    • Pulmonary Function Tests (PFTs)
    • Right Heart Catheterization
    • Six Minute Walk
    • Ventilation Perfusion Scan (VQ Scan)
    • CTEPH
      • CTEPH: WHO Group 4 Pulmonary Hypertension
      • PTE (Pulmonary Thromboendarterectomy) Surgery
      • Adempas used to Treat PAH and CTEPH
  • PAH Treatment
    • Pulmonary Hypertension Centers
    • Pulmonary Hypertension Treatments
    • Continuously Infused Therapies Used to Treat PH
    • Prostanoids for Treatment of PH
    • Adcirca and Revatio Used to Treat Pulmonary Arterial Hypertension (PAH)
    • Adempas used to Treat PAH and CTEPH
    • Tracleer, Letairis, and Opsumit Treatments
    • Oxygen Therapy for Pulmonary Hypertension
    • Salt and Water Restrictions
    • Exercise & PAH
    • Diuretics
    • Blood Thinners
    • Getting the Most Out of PAH Therapy
      • Letairis
      • Opsumit
      • Sildenafil (Revatio)
  • Research
  • FAQ’s
    • Implanted Remodulin Pump, Right Heart Catheterization, PAH & Pregnancy
    • Oral Treatments, Care Centers & Hole in Heart
    • FAQ’s: Altitude, Cold & Allergy Medications
    • FAQ’s: Psoriasis, Idiopathic PAH, Contraceptives & PAH
    • FAQ’s: Causes of Pulmonary Hypertension, Symptom Frequency & Care Centers
    • FAQ: PAH Experts, Pregnancy, Mild PAH & Vacationing
    • FAQ’s: CTEPH, Blood Clots, Corrective Surgery & PAH Care Centers
    • FAQ’s: VQ Scans & PAH Curable?
    • FAQ’s: Mild Pulmonary Hypertension?
    • FAQ’s: Boating, Swimming & Eating with PAH
    • FAQ’s: Borderline Pulmonary Hypertension, Hand Swelling, Children with PAH, Costs

November 18th is the First Ever CTEPH Awareness Day

November 13, 2014 By Dr. Jeremy Feldman

As part of PAH Awareness Month this year November 18th has been assigned as the official CTEPH Awareness Day. This will be the first ever awareness day focused on CTEPH or chronic thromboembolic pulmonary hypertension.

What Makes CTEPH Different from PAH?

CTEPH is caused by chronic blood clots in the lungs that lead to the increased pressure in the pulmonary arteries and the right side of the heart. It is the only form of PAH that can potentially be cured. The possible cure is a surgical procedure called a pulmonary thromboendarterectomy (PTE) that involves opening the chest and removing large areas of clot. This is an intense surgery and there are only a few centers in the country that perform it. Not every patient with CTPEH will qualify for an endarterectomy.

Medications that are approved for PAH are not necessarily indicated for CTEPH. The first medication to be approved by the FDA with a specific indication to be used in CTEPH was Adempas. This medication has been shown to improve exercise capacity and delay clinical worsening in patients with PAH and CTEPH. No other medications approved for PAH have proven to have these positive outcomes in CTEPH patients.

Why Does CTEPH Need Its Own Day?

Raising awareness for chronic thromboembolic pulmonary hypertension is extremely important because it is a potentially curable disease and there is now a specific medication approved to treat it. Currently CTEPH is much more prevalent than recognized meaning patients are walking around with the disease without the proper diagnosis. The goal of CTEPH Awareness Day is to increase awareness so that every patient with a diagnosis of PH is screened for chronic thromboembolic pulmonary hypertension. There are several tests that can be used to look for chronic clots in the lungs including a VQ scan (ventilation perfusion scan) and pulmonary angiography (usually performed at the time of the initial right heart catheterization).

If the diagnosis of CTEPH is missed a patient with a potentially curable disease may be subjected to expensive PAH therapies that have some difficult side effects without improvement. Like all PAH patients if not properly diagnosed and treated CTEPH will progress. Without treatment the chronic clots will block off blood flow to the lungs leading to heart failure and even death.

 3 Ways to Participate in CTEPH Awareness Day

  1. Learn about CTEPH. Visit our CTEPH page to learn more about the disease.
  2. Share your CTEPH story. Speak to friends, family acquaintances, co-workers, etc. about your personal CTEPH story along with information about screening for the disease and treatments.
  3. Use social media. Visit, like, follow, and share organizations on social media sites that are devoted to raising awareness about CTEPH.

Filed Under: Blog, Home Page, Living with PAH, PH Doctors & Centers, Pulmonary Hypertension Diagnosis, Pulmonary Hypertension Prognosis, Pulmonary Hypertension Treatments

PAH Life Expectancy

PAH Research

Research, Life Expectancy & Prognosis for PH

Major Developments in Pulmonary Hypertension Affecting Prognosis 1.     Approval of

Where to Get Treatment?

CCCs for PAH

Pulmonary Hypertension Centers

Where to get treatment for pulmonary hypertension? Pulmonary arterial hypertension is a

Popular Posts

Researching PH treatments

Scrotal Edema

By Dr. Jeremy Feldman

Swelling of the Scrotum with Pulmonary Arterial Hypertension. We recently received a great question about scrotal edema

researching stem cells to treat PAH

Buyer Beware: Stem Cells In PAH

By Dr. Jeremy Feldman

Have you seen the new ads promising to cure your ________ (you fill in the blank with whatever disease you have) with

good news in pah

 

Disclaimer

Recent Blog Posts

  • In Memoriam:  Greg Ahearn, MD June 16, 2024
  • Sotatercept (Winrevair) Approved! June 1, 2024
  • Disappointing News for Rodatristat Ethyl October 11, 2023

Categories

Archives