• Home
  • About Us
  • Blog

Pulmonary Hypertension RN

  • What is Pulmonary Hypertension?
    • What is Pulmonary Hypertension?
    • Pulmonary Hypertension Symptoms
    • Types of Pulmonary Hypertension
    • Causes of Pulmonary Hypertension
    • PH vs. PAH
    • Diastolic Heart Failure vs. PAH
    • WHO Group 3 Pulmonary Hypertension, IPF & COPD
    • Pulmonary Veno-Occlusive Disease
    • Hereditary Hemorrhagic Telangiectasia (HHT)
      • Hereditary Hemorrhagic Telangiectasia (HHT) Treatment
    • Functional Classification of Pulmonary Hypertension
    • Congenital Heart Disease
      • Eisenmenger’s Syndrome
      • Update on Management of PAH-CHD
      • Congenital Heart Disease & Sleep Apnea
      • Complex Congenital Heart Disease
      • Atrial Septal Defect and Pulmonary Arterial Hypertension
    • Pediatric Pulmonary Arterial Hypertension
    • Sickle Cell and Pulmonary Hypertension
    • Stimulant Associated Pulmonary Arterial Hypertension
    • Porto-Pulmonary Syndrome
    • Research, Life Expectancy & Prognosis for PH
  • Diagnosing & Monitoring PAH
    • Pulmonary Arterial Hypertension Diagnosis
    • How Am I Doing? Assessing Your PAH.
    • Blood Tests
    • Cardiopulmonary Exercise Test (CPET)
    • CT (Computed Tomography) Scan
    • Echocardiogram: An Overview
    • Echocardiogram: A Detailed Look
    • Pulmonary Function Tests (PFTs)
    • Right Heart Catheterization
    • Six Minute Walk
    • Ventilation Perfusion Scan (VQ Scan)
    • CTEPH
      • CTEPH: WHO Group 4 Pulmonary Hypertension
      • PTE (Pulmonary Thromboendarterectomy) Surgery
      • Adempas used to Treat PAH and CTEPH
  • PAH Treatment
    • Pulmonary Hypertension Centers
    • Pulmonary Hypertension Treatments
    • Continuously Infused Therapies Used to Treat PH
    • Prostanoids for Treatment of PH
    • Adcirca and Revatio Used to Treat Pulmonary Arterial Hypertension (PAH)
    • Adempas used to Treat PAH and CTEPH
    • Tracleer, Letairis, and Opsumit Treatments
    • Oxygen Therapy for Pulmonary Hypertension
    • Salt and Water Restrictions
    • Exercise & PAH
    • Diuretics
    • Blood Thinners
    • Getting the Most Out of PAH Therapy
      • Letairis
      • Opsumit
      • Sildenafil (Revatio)
  • Research
  • FAQ’s
    • Implanted Remodulin Pump, Right Heart Catheterization, PAH & Pregnancy
    • Oral Treatments, Care Centers & Hole in Heart
    • FAQ’s: Altitude, Cold & Allergy Medications
    • FAQ’s: Psoriasis, Idiopathic PAH, Contraceptives & PAH
    • FAQ’s: Causes of Pulmonary Hypertension, Symptom Frequency & Care Centers
    • FAQ: PAH Experts, Pregnancy, Mild PAH & Vacationing
    • FAQ’s: CTEPH, Blood Clots, Corrective Surgery & PAH Care Centers
    • FAQ’s: VQ Scans & PAH Curable?
    • FAQ’s: Mild Pulmonary Hypertension?
    • FAQ’s: Boating, Swimming & Eating with PAH
    • FAQ’s: Borderline Pulmonary Hypertension, Hand Swelling, Children with PAH, Costs

Winter Weather Causes Shipping Delays For PAH Medications

January 22, 2014 By Dr. Jeremy Feldman

The United States is getting hit with brutal severe winter weather this year and the country held their breath when UPS and FedEx stated that they could not fulfill their Christmas shipping deadlines.  These delays affect the specialty pharmacies shipping directly to pulmonary arterial hypertension patients as well as suppliers shipping to your local pharmacies.Delivery of PAH medications So what can a pulmonary hypertension patient do if their Letairis, Remodulin, or Opsumit shipment is delayed?  Follow the simple steps below to get through this shipping crisis and avoid anxiety over future shipments.

Order Your PH Medications Ahead Of Time

Most insurance companies will have a set number of days they demand between refills.  Know when your insurance and pharmacy will allow you to refill.  Mark this timeline on your calendar and refill the first day you are allowed.  Always know the supply of PAH medication that you have on hand and avoid being surprised when there isn’t another package or bottle of medication to open.

Many specialty pharmacies will contact patients to process refills. Do not wait for them to contact you.  This may be a luxury if the timing works out and they call you just when you were thinking about calling them but do not hang the success of your PH treatment on their outbound phone call.  Pick up the phone and call.  This also applies to local pharmacies that have auto refill services.  It is better to plan on everyone else being delayed or unorganized and then be pleasantly surprised when they are on the ball than to go without your PAH treatment.

Make An Emergency Back Up Kit

Always have an emergency back up kit of medication and supplies that you do not count when taking inventory.  Most specialty pharmacies will help set this kit up for you when they show you how  to administer the complex infused or inhaled therapies.  If you are not on a complex therapy with a specialty pharmacy work with your physicians office on what you would need for an emergency back up medication kit.

For most patients an extra 1-2 days of medications should suffice but if you live in a remote area you may need a larger supply.

Always remember to switch out the medications in the emergency back up kit so that they don’t expire.

Notify Your Physicians Office Right Away

Notify your nurse coordinator right away if you are aware of a delay in shipment.  Many pulmonary hypertension centers have samples or ways of getting you the medications you need in a timely manner.  The earlier they know about the problem the better the chances of them being able to solve it prior to it affecting your PAH.  The physician’s office can also advise you on how many, if any, doses they are comfortable with you missing.  Always error on the side of contacting your physician, call even if you think you will most likely squeak by.

Know The Closest Facility With PH Medications In Stock

Work with your pulmonary hypertension specialist to find out what facilities have PH medications in stock.  Pulmonary arterial hypertension is a rare disease and the medications are expensive so most hospitals do not routinely stock them.   If all other options fail and you are unable to obtain your therapy, particularly continuously infused therapies, you may need to present to the closest facility with the medication in stock.  Often they will be able to provide a fill of your cartridge or cassette and send you on your way.  This is very rarely necessary for patients taking oral therapies as samples or alternative medications in the same class can usually be found, but it is imperative to never discontinue a continuously infused therapy abruptly as this may cause rebound pulmonary arterial hypertension and be life threatening. Always contact your physician to alert them of the situation and remember to bring your dosing sheet and other supplies such as cassettes or syringes for your particular pump.

Filed Under: Blog, Home Page, Living with PAH, Pulmonary Hypertension Treatments

PAH Life Expectancy

PAH Research

Research, Life Expectancy & Prognosis for PH

Major Developments in Pulmonary Hypertension Affecting Prognosis 1.     Approval of

Where to Get Treatment?

CCCs for PAH

Pulmonary Hypertension Centers

Where to get treatment for pulmonary hypertension? Pulmonary arterial hypertension is a

Popular Posts

pulmonary hypertension related lung disease

Pulmonary Hypertension and Interstitial Lung Disease

By Dr. Jeremy Feldman

Pulmonary hypertension (elevated pressure within the blood vessels of the lungs) is organized into five groups: Group

PAH patient

How Am I Doing? Assessing Your PAH.

By Dr. Jeremy Feldman

Perhaps the most common question that I get asked by my patients is “How am I doing”.  This is both a simple and a

good news in pah

 

Disclaimer

Recent Blog Posts

  • In Memoriam:  Greg Ahearn, MD June 16, 2024
  • Sotatercept (Winrevair) Approved! June 1, 2024
  • Disappointing News for Rodatristat Ethyl October 11, 2023

Categories

Archives